circRNA basic information
circBase ID: hsa_circ_0000284
Name: hsa_circ_HIPK3
Synonym: -
Host Gene: HIPK3
Genomic location(hg19): chr11:33307958-33309057:+
Genomic location(hg38): chr11:33286412-33287511:+
Subcellular localization: cytoplasm
 
 
 
 
 
 
 
Disease basic information
MONDO ID:
0002771
MONDO name: pulmonary fibrosis
Disease details: pulmonary fibrosis
Disease DO ID:
3770
Disease MeSH ID:
D011658
Disease NCIt ID:
C26869
Disease ICD11 ID:
-
Disease OMIM ID:
-
Species: Human
Species details: Homo sapiens
Tissue specimen:

lung

Cell lines:

WI-38; HEK-293T

In vivo animal model:

other disease animal model

circRNA-disease information
Expression pattern:
UP
Associated gene: Ago2, SOX4, COL1A1
Associated microRNA: miR-338-3p
Biological function: Promotes fibroblast-to-myofibroblast transition (FMT) and fibroblast proliferation; its silencing attenuates pulmonary fibrosis and ECM/collagen deposition.
Molecular mechanism: Acts as a competing endogenous RNA (miRNA sponge) for miR-338-3p in an Ago2-dependent manner, relieving repression of SOX4 and COL1A1 and thereby promoting FMT.
Biological pathway or process:

proliferation (promotes); EMT (promotes); ceRNA regulation (promotes)

Detected method:
Q
H
Validation methods:

divergent primers PCR; RNase R Treatment; Sanger Sequencing; RT-qPCR; FISH / smFISH; RIP (RNA Immunoprecipitation); Luciferase Reporter Assay; Transfection; EdU Staining; CCK8; Western Blot; IF (Immunofluorescence); In Vivo Animal Model; H&E Staining

Clinical significance:

Upregulated in lung tissue samples of patients with idiopathic pulmonary fibrosis.

Description:

circHIPK3 is up-regulated in bleomycin-induced pulmonary fibrosis, TGF-beta1-induced fibroblast-to-myofibroblast transition, and IPF patient lungs. It promotes FMT and fibroblast proliferation by sponging miR-338-3p (Ago2-dependent), increasing SOX4 and COL1A1 expression; circHIPK3 knockdown alleviates fibrosis in vivo.

Confidence score:

0.7663

Other information
Title:

circHIPK3 regulates lung fibroblast-to-myofibroblast transition by functioning as a competing endogenous RNA.

Journal: Cell death & disease
Published: 2019
PubMed ID: 30796204
Study type:

combined biological and clinical study

Data availability: Supplementary Information accompanies this paper at (10.1038/s41419-019-1430-7).
Code availability: -