circRNA basic information
circBase ID: hsa_circ_0002805
Name: hsa_circ_ZBTB46
Synonym: circZBTB46
Host Gene: ZBTB46
Genomic location(hg19): chr20:62407030-62422143:-
Genomic location(hg38): chr20:63775677-63790790:-
Subcellular localization: nucleus and cytoplasm
 
 
 
 
 
 
 
Disease basic information
MONDO ID:
0005350
MONDO name: abdominal aortic aneurysm
Disease details: abdominal aortic aneurysm / AAA
Disease DO ID:
7693
Disease MeSH ID:
D017544
Disease NCIt ID:
-
Disease ICD11 ID:
1154633768
Disease OMIM ID:
-
Species: Human
Species details: Homo sapiens
Tissue specimen:

human abdominal aortic aneurysm tissues; normal aortic tissues; human blood vessels; human renal arteries

Cell lines:

human aortic VSMCs

In vivo animal model:

-

circRNA-disease information
Expression pattern:
UP
Associated gene: PDLIM5, Smad2, COL1A2, KLF4, TGF-beta, Smad3
Associated microRNA: -
Biological function: circZBTB46 inhibits TGF-beta-induced Smad signaling and downregulates COL1A2/type I collagen synthesis in human vascular smooth muscle cells, contributing to vascular homeostasis and aneurysm development.
Molecular mechanism: circZBTB46 acts through a protein-scaffold mechanism by binding PDLIM5 and mediating the PDLIM5-Smad2 interaction, thereby inhibiting TGF-beta/Smad signaling and reducing COL1A2 expression.
Biological pathway or process:

TGF-beta/SMAD (inhibits); other pathway/process (inhibits)

Detected method:
Q
H
S
Validation methods:

Back-Splice Junction PCR / divergent primers PCR; Sanger Sequencing; RT-qPCR; FISH / smFISH; Clinical Sample Validation; RIP (RNA Immunoprecipitation); RNA Pull-Down; Co-IP; Transfection; Western Blot; IF (Immunofluorescence); H&E Staining

Clinical significance:

circZBTB46 expression is increased in human AAA tissues and may represent a potential target for TGF-beta-induced ECM remodeling.

Description:

circZBTB46 is a human ZBTB46-derived circRNA that is increased in abdominal aortic aneurysm tissues. In VSMCs, it binds PDLIM5 and promotes the PDLIM5-Smad2 interaction, inhibiting TGF-beta/Smad signaling and suppressing COL1A2/type I collagen expression, suggesting a role in vascular ECM remodeling and aneurysm development.

Confidence score:

0.8115

Other information
Title:

Down-regulation of the Smad signaling by circZBTB46 via the Smad2-PDLIM5 axis to inhibit type I collagen expression.

Journal: Journal of geriatric cardiology : JGC
Published: 2023
PubMed ID: 37416515
Study type:

combined biological and clinical study

Data availability: -
Code availability: -