circRNA basic information
circBase ID: hsa_circ_0028912
Name: hsa_circ_RNF10
Synonym: circRNF10
Host Gene: RNF10
Genomic location(hg19): chr12:121004627-121009094:+
Genomic location(hg38): chr12:120566824-120571291:+
Subcellular localization: cytoplasm
 
 
 
 
 
 
 
Disease basic information
MONDO ID:
0018177
MONDO name: glioblastoma
Disease details: glioblastoma / GBM
Disease DO ID:
3068
Disease MeSH ID:
D005909
Disease NCIt ID:
C3058
Disease ICD11 ID:
-
Disease OMIM ID:
-
Species: Human
Species details: Homo sapiens
Tissue specimen:

glioma tissue; glioblastoma tissues; normal brain tissue

Cell lines:

SYNS03; SYNS05; SYNS06; SYNS08

In vivo animal model:

cell line-derived xenograft

circRNA-disease information
Expression pattern:
UP
Associated gene: ZBTB48, MKRN3, IGF2BP3, HSPB1
Associated microRNA: -
Biological function: Promotes glioblastoma progression by enhancing GSC proliferation and stemness and enabling ferroptosis evasion (ferroptosis resistance), including lowering Fe2+ accumulation.
Molecular mechanism: circRNF10 binds ZBTB48 and increases its protein stability by reducing MKRN3-mediated K48-linked ubiquitination; ZBTB48 transcriptionally upregulates HSPB1 and IGF2BP3; IGF2BP3 binds circRNF10 to enhance its RNA stability, forming a circRNF10/ZBTB48/IGF2BP3 positive feedback loop that remodels iron metabolism and suppresses ferroptosis.
Biological pathway or process:

proliferation (promotes); stemness (promotes); ferroptosis (inhibits); mitochondrial function (other); iron metabolism (other)

Detected method:
Q
S
Validation methods:

RT-qPCR; Back-Splice Junction PCR / divergent primers PCR; Sanger Sequencing; RNase R Treatment; FISH / smFISH; Nuclear-Cytoplasmic Fractionation; Clinical Sample Validation; RNA Pull-Down; RIP (RNA Immunoprecipitation); Co-IP; ChIP / ChIP-seq; Luciferase Reporter Assay; Actinomycin D / DRB Stability Assay; Transfection; MTT; EdU Staining; Cell Cycle Assay; Western Blot; In Vivo Animal Model; IHC (Immunohistochemistry); Survival Analysis; Bioinformatics Analysis; ubiquitination; RNA-seq

Clinical significance:

circRNF10 is positively correlated with glioma grade and high circRNF10 expression is associated with poor prognosis.

Description:

circRNF10 (hsa_circ_0028912) is up-regulated in glioblastoma/glioma and high expression associates with poor prognosis. It promotes GSC proliferation and stemness by inhibiting ferroptosis and remodeling iron metabolism, via binding/stabilizing ZBTB48 (through blocking MKRN3-mediated ubiquitination) and forming a positive feedback loop with ZBTB48-driven IGF2BP3 and IGF2BP3-mediated circRNF10 stabilization, with downstream HSPB1 upregulation.

Confidence score:

0.8991

Other information
Title:

CircRNF10 triggers a positive feedback loop to facilitate progression of glioblastoma via redeploying the ferroptosis defense in GSCs.

Journal: Journal of experimental & clinical cancer research : CR
Published: 2023
PubMed ID: 37723588
Study type:

combined biological and clinical study

Data availability: GSE165926; TCGA; CGGA
Code availability: -