circRNA basic information
circBase ID: hsa_circ_0037100
Name: hsa_circ_PCSK6
Synonym: circPCSK6
Host Gene: PCSK6
Genomic location(hg19): chr15:101929668-101970268:-
Genomic location(hg38): chr15:101389463-101430063:-
Subcellular localization: cytoplasm
 
 
 
 
 
 
 
Disease basic information
MONDO ID:
0003210
MONDO name: intrahepatic cholangiocarcinoma
Disease details: intrahepatic cholangiocarcinoma / ICC
Disease DO ID:
4928
Disease MeSH ID:
-
Disease NCIt ID:
C35417
Disease ICD11 ID:
1253728223; 387909164
Disease OMIM ID:
-
Species: Human
Species details: Homo sapiens
Tissue specimen:

tumor tissues; paired normal tissues; adjacent normal tissues; wild-type (WT) liver tissue; primary ICC mouse tissues

Cell lines:

RBE; HuCCT1; KMBC; CCLP-1; HIBECs

In vivo animal model:

patient-derived xenograft; cell line-derived xenograft; genetically engineered animal model

circRNA-disease information
Expression pattern:
DN
Associated gene: EIF4A3
Associated microRNA: -
Biological function: Inhibits tumor cell proliferation, migration, invasion, stemness, and metastasis; promotes apoptosis; enhances sensitivity to gemcitabine.
Molecular mechanism: circPCSK6 encodes circPCSK6-167aa; this peptide regulates IkappaBalpha ubiquitination and inhibits NF-kappaB activation; circPCSK6 is negatively regulated by EIF4A3 via binding/splicing control.
Biological pathway or process:

NF-kappaB (inhibits); proliferation (inhibits); apoptosis (promotes); migration (inhibits); invasion (inhibits); metastasis (inhibits); stemness (inhibits); drug resistance (inhibits)

Detected method:
Q
Validation methods:

Bioinformatics Analysis; RT-qPCR; Back-Splice Junction PCR / divergent primers PCR; Sanger Sequencing; RNase R Treatment; Actinomycin D / DRB Stability Assay; Nuclear-Cytoplasmic Fractionation; FISH / smFISH; Clinical Sample Validation; EdU Staining; Transwell Assay; TUNEL; Western Blot; In Vivo Animal Model; H&E Staining; IHC (Immunohistochemistry); Transfection; RIP (RNA Immunoprecipitation); ROC Analysis; Survival Analysis

Clinical significance:

Lower circPCSK6 expression is correlated with unfavorable patient outcomes and adverse prognosis in ICC.

Description:

circPCSK6 (hsa_circ_0037100), derived from the PCSK6 gene, is down-regulated in intrahepatic cholangiocarcinoma and acts as a tumor suppressor. It exerts major effects via its encoded peptide circPCSK6-167aa, which inhibits NF-kappaB signaling by stabilizing IkappaBalpha through reduced ubiquitination, and its expression is negatively regulated by the RBP EIF4A3.

Confidence score:

0.8671

Other information
Title:

A Novel 167-Amino Acid Protein Encoded by CircPCSK6 Inhibits Intrahepatic Cholangiocarcinoma Progression via IKBalpha Ubiquitination.

Journal: Advanced science (Weinheim, Baden-Wurttemberg, Germany)
Published: 2025
PubMed ID: 39836545
Study type:

combined biological and clinical study

Data availability: GSE181523
Code availability: -