circRNA basic information
circBase ID: hsa_circ_0000230
Name: hsa_circ_ZEB1
Synonym: circZEB1 / circZBE1
Host Gene: ZEB1
Genomic location(hg19): chr10:31661946-31750166:+
Genomic location(hg38): chr10:31373017-31461237:+
Subcellular localization: cytoplasm
 
 
 
 
 
 
 
Disease basic information
MONDO ID:
0018177
MONDO name: glioblastoma
Disease details: glioblastoma / GBM
Disease DO ID:
3068
Disease MeSH ID:
D005909
Disease NCIt ID:
C3058
Disease ICD11 ID:
-
Disease OMIM ID:
-
Species: Human
Species details: Homo sapiens
Tissue specimen:

glioma tissue; glioblastoma tissue; adjacent normal brain tissue (NBT); tumor tissue

Cell lines:

GSC103; GSC107; GSC108; GSC109; GSC111; GSC112

In vivo animal model:

cell line-derived xenograft

circRNA-disease information
Expression pattern:
UP
Associated gene: LBH, TNF-alpha, NF-kappaB signaling pathway, FUS, AGO2
Associated microRNA: hsa-miR-128-3p
Biological function: promotes malignant phenotype and stemness of GSCs, including cell viability/proliferation, invasion, self-renewal and tumorigenesis
Molecular mechanism: circZEB1 acts as a ceRNA sponge for miR-128-3p to upregulate LBH; LBH increases TNF-alpha transcription and activates NF-kappaB signaling; LBH upregulates FUS, which binds circZEB1 and maintains its stability, forming a positive feedback loop
Biological pathway or process:

NF-kappaB (promotes); proliferation (promotes); invasion (promotes); stemness (promotes); ceRNA regulation (promotes)

Detected method:
Q
M
Validation methods:

Microarray; RT-qPCR; RNase R Treatment; Sanger Sequencing; FISH / smFISH; Luciferase Reporter Assay; RIP (RNA Immunoprecipitation); RNA Pull-Down; Actinomycin D / DRB Stability Assay; Transfection; MTT; EdU Staining; Transwell Assay; Western Blot; ELISA; IHC (Immunohistochemistry); In Vivo Animal Model; H&E Staining; Survival Analysis; Bioinformatics Analysis; Clinical Sample Validation

Clinical significance:

High circZEB1 expression correlates with higher tumor grade and shorter survival; proposed as a biomarker/target for GBM therapy

Description:

circZEB1 is up-regulated in GBM and GSCs and promotes proliferation, invasion, stemness, and in vivo tumorigenesis. It functions as a miR-128-3p sponge to increase LBH, which enhances TNF-alpha and activates NF-kappaB signaling; LBH also increases FUS, and FUS binds circZEB1 to stabilize it, forming a positive feedback loop.

Confidence score:

0.8871

Other information
Title:

FUS/circZEB1/miR-128-3p/LBH feedback loop contributes to the malignant phenotype of GSCs via TNF-alpha-mediated NF-kappaB signaling pathway.

Journal: Cancer cell international
Published: 2024
PubMed ID: 39511561
Study type:

combined biological and clinical study

Data availability: GSE109569
Code availability: -